Table 2

Clinical characteristics of the children diagnosed with an inherited cardiac arrhythmia syndrome

Children diagnosed with an inherited cardiac arrhythmia syndrome (n=47)
Time since diagnosis, days
 Mean (SD)1444.31 (1062.27)
 Minimum/maximum (range)42/4678 (4636)
Diagnosis, n (%)
 Long QT syndrome29 (62)
 Brugada syndrome11 (23)
 Catecholaminergic polymorphic ventricular tachycardia5 (11)
 Short QT syndrome1 (2)
 Unknown1 (2)
Symptoms, n (%)
 No27 (57)
 Yes20 (43)
Out-of-hospital cardiac arrest, n (%)
 No44 (94)
 Yes3 (6)
Treatment, n (%)
 None13 (28)
 Medication27 (57)
 Medication+ICD7 (15)
History of SCD in immediate family, n (%)
 No41 (87)
 Yes6 (13)
  • ICD, implantable cardioverter-defibrillator; SCD, sudden cardiac death.