Children diagnosed with an inherited cardiac arrhythmia syndrome (n=47) | |
Time since diagnosis, days | |
Mean (SD) | 1444.31 (1062.27) |
Minimum/maximum (range) | 42/4678 (4636) |
Diagnosis, n (%) | |
Long QT syndrome | 29 (62) |
Brugada syndrome | 11 (23) |
Catecholaminergic polymorphic ventricular tachycardia | 5 (11) |
Short QT syndrome | 1 (2) |
Unknown | 1 (2) |
Symptoms, n (%) | |
No | 27 (57) |
Yes | 20 (43) |
Out-of-hospital cardiac arrest, n (%) | |
No | 44 (94) |
Yes | 3 (6) |
Treatment, n (%) | |
None | 13 (28) |
Medication | 27 (57) |
Medication+ICD | 7 (15) |
History of SCD in immediate family, n (%) | |
No | 41 (87) |
Yes | 6 (13) |
ICD, implantable cardioverter-defibrillator; SCD, sudden cardiac death.