Primary defects in lung branching morphogenesis, resulting in neonatal lethal pulmonary
hypoplasias, are incompletely understood. To elucidate the pathogenetics of human lung …

Objectives Lumacaftor–ivacaftor is a cystic fibrosis transmembrane conductance regulator
(CFTR) modulator known to improve clinical status in people with cystic fibrosis (CF). The …

Background Atopic march refers to the typical transition from a food allergy in early
childhood to allergic asthma in older children and adults. However the precise interplay of …

Only few studies report long-term evolution of patients with neuroendocrine cell hyperplasia
of infancy (NEHI). We report data from a 54-patient cohort followed up in the French network …

Methods This retrospective before/after study design was conducted in the general
paediatric unit of a tertiary care French hospital, looking at 1 year before (ie, the winter of …

Early diagnosis of neuroendocrine cell hyperplasia of infancy (NEHI) is crucial as,
conversely to the other causes of intersititial lung disease, corticosteroids are not …

We investigated the in vitro susceptibility of ceftazidime-avibactam (CZA) resistant
Stenotrophomonas maltophilia to the associations aztreonam/amoxicillin-clavulanate (ATM …

Background The two pediatric cystic fibrosis centers (CFCs) in Paris (Robert Debré) and
Nantes, France, have been developing therapeutic patient education (TPE) programs since …

Epidemiological data suggest a link between food allergies and the subsequent
development of asthma. Although this progression may result from the additional effects of …

Polyhydramnios is a recurrent clinical concern. Excessive amniotic fluid can be caused by
an imbalance between its production and its removal, and is associated with an increased …